How Long Is the Life Expectancy of Muir-Torre Syndrome?

Q:
How long is the life expectancy of Muir-Torre syndrome?
A:
Muir-Torre syndrome (MTS) is a form of Lynch syndrome which is an autosomal dominant genetic condition. MTS is characterized by sebaceous (oil gland) skin tumors in association with internal cancers. The most common internal site involved is the gastrointestinal tract, followed by the genitourinary tract.
The most characteristic signs of MTS is sebaceous adenoma. Other types of skin tumors in affected people include sebaceous epitheliomas, sebaceous carcinomas (which commonly occur on the eyelids) and keratoacanthomas.
In terms of the life expectancy, about 60% of people with MTS develop metastatic disease. Prognosis may depend on the associated internal cancer(s) each affected person has.
If you still have any questions, please discuss them with your doctor.
Keywords: Muir-Torre syndrome

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